Data Last Updated: June 9, 2025

NAACCR Item #3917: Primary Sclerosing Cholangitis

Item # Length Source of Standard Section Name Year Implemented Version Implemented XML NAACCR ID Parent XML Element
3917 1 NAACCR Stage/Prognostic Factors 2018 18 primarySclerosingCholangitis Tumor
Required Status:

NPCR Collect: No recommendation
CoC Collect: Required, site specific
SEER Collect: No recommendation
CCCR Collect: No recommendation

Description
Primary sclerosing cholangitis denotes a chronic autoimmune inflammation of the bile ducts that leads to scar formation and narrowing of the ducts over time. It is a prognostic factor for intrahepatic bile duct cancer.
Rationale
Primary Sclerosing Cholangitis is a Registry Data Collection Variable in AJCC. This data item was previously collected for Intrahepatic Bile Duct, SSF# 11.
Allowable Values
0, 1, 8, 9
Codes
Code Description
0 PSC not identified/not present
1 PSC present
8 Not applicable: Information not collected for this case (If this information is required by your standard setter, use of code 8 may result in an edit error.)
9 Not documented in medical record PSC not assessed or unknown if assessed
Code Notes
Each Site-Specific Data Item (SSDI) applies only to selected primary sites, histologies, and years of diagnosis. Depending on applicability and standard-setter requirements, SSDIs may be left blank.